A 27-year-old man presents to the emergency department with chest pain and hemoptysis. His past medical history is significant for chronic sinusitis and several bouts of pneumonia that have required hospitalizations. In family history, you discover that he and his wife have not been able to have kids because of his infertility. In the physical examination, you were surprised to hear heart sounds on the right side of the chest. Later he informs you that his heart is on the right side. Pulmonary function tests (PFTs) reveal a decreased FEV1/FVC ratio. CT scan reveals dilated bronchioles with signet-ring appearance and situs inversus. Of the following, which is the most likely diagnosis in this patient?
