Key Points  Granulomatosis with polyangiitis is a systemic necrotizing, mostly small vessel vasculitis of unknown etiology that manifests as granulomatous lesions of the upper respiratory tract, lungs and kidneys.  -Formerly known as Wegener Granulomatosis, it was renamed because of the eponymous individual’s association with Nazism  -GPA is the most common form of vasculitis to involve […]